SUMMARY
Osteopetrosis is a rare hereditary condition which may have autosomal recessive or autosomal dominant inheritance. Patients tend to present most commonly with fractures but involvement of cranial nerves and hematopoetic system is not uncommon. In fact, patients with infantile and intermediate type tend to present more often with problems other than orthopaedic problems. While diagnosis can be made on the basis of radiographs, management needs to be customized for every patient. Non operative and operative management both have their advantages and disadvantages. We are here reporting a case of subtrochanteric fracture in an eight-year-old child which was managed successfully with a dynamic hip screw (DHS) after closed reduction was unsuccessful. Surgery could be performed successfully by taking precautions during reduction, drilling and screw placement. At the latest follow up, which was after one and half years of surgery the fracture had united well and the child faced no limitations of activities. Thus, a DHS can be considered as effective mean of management of pediatric subtrochanteric fractures in osteopetrosis.